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Case Report
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| Solid (Type 3) pleuropulmonary blastoma | ||||||
| Luvo Gaxa1, Bafana Hlatshwayo2, Aletta Lefentse Motene3 | ||||||
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1MBChB, MMed (Rad D), Paediatric Radiology fellow, Diagnostic Radiology and Imaging, R, South Africa.
2Dip Rad Diag, MBChB, MMed Rad D, Senior Specialist, Diagnostic Radiology and Imaging, Polokwane-Mankweng Hospital Complex, Polokwane, Limpopo, South Africa. 3MBchB, Fc Paed, Fellow in Paediatric Pulmonology, Senior Specialist, Paediatrics, Polokwane-Mankweng Hospital Complex, Polokwane, Limpopo, South Africa. | ||||||
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| How to cite this article: |
| Gaxa L, Hlatshwayo B, Motene AL. Solid (Type 3) pleuropulmonary blastoma. Case Rep Int 2017;6:1–4. |
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Abstract
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Introduction:
Pleuropulmonary blastoma is a rare solid and/or cystic progressive and aggressive malignant intra-thoracic tumor of childhood which belongs to a group of dysontogenetic neoplasms such as Wilms tumor, neuroblastoma and hepatoblastoma. The incidence of pleuropulmonary blastoma ranges between 0.25 and 0.5% of primary lung tumors making this entity a rare primary malignant lung tumor.
Case Report: A two-month-old male neonate was referred from a regional hospital with a three-day history of cough, fever and shortness of breath. No previous medical history reported. The patient was delivered at term through a normal vaginal delivery which was uneventful. Birth weight 3 kg, length 48 cm, Apgar score 10/10 and the head circumference was 35 cm. The patient's retro-viral disease status was negative. On percussion there was dullness and bilateral crepitations. There was bilateral decreased air-entry. No signs of cardiac failure. The rest of the systems were within normal limits. The arterial blood gases showed respiratory acidosis with hypoxia. Chest X-ray showed a white out of the right hemithorax and CT scan of the chest showed a large soft tissue mass in the right hemithorax associated with free fluid in the right hemithorax and the biopsy was performed which confirmed the diagnosis of a pleuropulmonary blastoma. The pleuropulmonary blastoma was a solid type (Type 3). Conclusion: Pleuropulmonary blastoma poses a diagnostic challenge because it does not have specific clinical or radiological features. The late diagnosis and delayed treatment of pleuropulmonary blastoma are associated with a deadly prognosis. | |
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Keywords:
Biopsy, Pleuropulmonary blastoma, Solid, Type 3, Types
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Author Contributions
Luvo Gaxa – Substantial contributions to conception and design, Acquisition of data, analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published Bafana Elliot Hlatshwayo – Substantial contributions to conception and design, Revising it critically for important intellectual content, Final approval of the version to be published Aletta Lefentse Motene – Substantial contributions to conception and design, Analysis and interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© 2017 Luvo Gaxa et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information. |
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